Taussig congenital heart disease center in her honor, and in 2005 the johns hopkins school of medicine named one of its four colleges in her honor. American pediatrician and embryologist noted for her work on congenital defects of the heart. Any information contained in this pdf file is automatically generated from digital material. Taussigbing anomaly, transposition of the great arteries, arterial. The study of taussigbing anomaly has been mentioned in research publications which can be found using our bioinformatics tool below.
In 1950, the similar case was reported, and the anomaly was eventually named the taussig bing heart 2. Results of arterial switch operation for primary total correction of the taussigbing anomaly. This anomaly was initially described in 1949 as transposition of the great. Read singlestage neonatal repair of taussigbing anomaly, operative techniques in thoracic and cardiovascular surgery on deepdyve, the largest online rental service for scholarly research with thousands of academic publications available at your fingertips.
Although substantial improvement has since been achieved in surgical results of the repair of the anomaly, management of the taussigbing anomaly remains challenging. There is a doubleoutlet right ventricle rv with the vsd arrows lying in a subpulmonary position. Arterial switch operation in patients with taussig bing anomaly our experience in coronary anatomy and staged repair. The taussigbing anomaly is relatively rare and it accounted for approximately 8% of cases in sridaromont series. Wilkinson, tiow goh, brian edis, samuel menahem, lance fong, robert weintraub. Bing is a cyanotic congenital heart disease characterized by the dual presence of a subpulmonic ventricular septal defect vsd along with a double outlet right ventricle dorv. Intraventricular baffle with arterial switch procedure, rev procedure. Pdf quantitative anatomy of taussigbing anomaly researchgate. Several modifications of this operation and advances in postoperative management have improved the surgical results, despite the application of the fontan approach to. Some authors prefer to include all cases of juxtapulmonary vsd with misalignment of infundibular septum under the rubric of taussigbing complex, possibly because of common features necessitating similar surgical options 2. Double outlet right ventricle dorv taussig bing malformation tetralogy of fallot with extreme dextroposition of the aorta eisenmengers anomaly eisenmenger ventricular septal defect european paediatric cardiac code reference of double outlet right ventricle is 01. This is one of the most complicated diseases in pediatric cardiology.
Consequently, single stage repair has become the preferred treatment method in most pediatric cardiac centers. His parents were middle class people, but luckily they managed to obtain medicare help from government. The icd10cm alphabetical index is designed to allow medical coders to look up various medical terms and connect them with the appropriate icd codes. Quantitative anatomy of taussigbing anomaly leo a bockeria 1, osman a makhachev 1,2, margarita v gorgeeva 1, marina s panova 1, t atiana y u philippkina 1, titalav kh khiriev 1 and sergey b. Read more about symptoms, diagnosis, treatment, complications. Twentythreeyear experience with the arterial switch. Between november 2006 and november 2015, 39 neonates with taussigbing anomaly and aortic.
Taussigbing is one of the variants of the double outlet right ventricle. Hemodynamic and angiographic findings following arterial switch repair for complete transposition volume 6 issue 4 arun srinivas, madathil ranjit, james l. This report contributes significantly to the aggregate surgical experience with this uncommon disease and continues to. Endothelin1 may play an important role in the fontan. Almost 50% of patients with taussigbing anomaly have aortic arch obstruction. Singlestage correction for taussigbing anomaly associated with. Taussigbing anomaly is a rare congenital heart malformation that was first described in 1949 by helen b. A new new testament welcome to my web site hal taussig.
Original drawing of the heart shows the size and position of the aorta and pulmonary artery and their relation to the septal defect. Taussigbing anomaly is one type of double outlet right ventricle and based congenital heart defects with a transposition of the great arteries tga and a sub. Coarctation in taussigbing malformation of the heart. Anatomical correction for complete transposition and. Addi tional aortopulmonary anastomosis for subaortic obstruction in the rastelli type repair of the taussigbing.
Surgical results of arterial switch operation for taussig. There are 0 terms under the parent term taussig bing syndrome in the icd10cm alphabetical index. Taussigbing anomaly the annals of thoracic surgery. This anomaly was initially described in 1949 as transposition of the great arteries 1. The aorta ao is distant from the left ventricle lv and anatomical repair by vsd closure is not possible. Hemodynamic and angiographic findings following arterial. Outcome of total correction of taussig bing anomaly. Current corrective surgical approaches for the taussigbing heart include arterial switch with ven tricular septal defect vsd closure and intraventricular repair as. When a baby is still in the womb, something goes wrong during the formation of the heart and both great arteries are attached to the right ventricle. The taussigbing anomaly turns 65 the journal of thoracic and.
Since fontan and baudet first described their procedure for the correction of tricuspid atresia in 1971, patients with singleventricle sv physiology have been treated with the fontan procedure. Advances in perioperative care, perfusion and surgical techniques have allowed the performance of complete repair of taussigbing anomaly with excellent results. Taussigbing anomaly american journal of cardiology. Aorta and pulmonary arteries were rising from the right ventricle and the ventricular septal defect was the only connection of the system detected with the left. Quantitative anatomy of taussigbing anomaly longdom. The article in this issue of the journal by vergnat and colleagues reports the largest singleinstitution experience with the surgical treatment of doubleoutlet right ventricle dorv with subpulmonary ventricular septal defect vsd, also known as the taussig bing anomaly. Singlestage neonatal repair of taussigbing anomaly. Within a few days after birth, he was diagnosed to be a blue baby. This study identifies the impact of the position of the great arteries and use of a staged surgical approach on the outcome after the arterial switch operation in children with taussigbing anomaly. The aim of the study was to analyse the longterm outcome of correction of the taussigbing heart. Attention program directors, faculty, residents, and fellows.
This is similar in many ways to transposition with a vsd and it may be treated with an arterial switch operation along with a patch within the. Taussigbing syndrome complete transposition of the aorta with a leftsided pulmonary artery overriding the left ventricle and ventricular septal defect, right ventricular hypertrophy, anteriorly situated aorta, and posteriorly situated pulmonary artery. The aim of the study was to analyse the longterm o. Tcell lymphoma, cutaneous other than mycosis fungoides tdp. Thirty three patients were followed up after anatomical correction of transposition of the great arteries or double outlet right ventricle and subpulmonary ventricular septal defect taussigbing anomaly. Synonyms for taussigbing syndrome in free thesaurus. Research of taussigbing anomaly has been linked to transposition of great vessels, double outlet right ventricle, ventricular septal defects, heart septal defects, congenital heart defects. The arterial switch operation aso is the method of choice for the taussigbing heart. Taussig was a member of several prestigious professional societies during her career. In these cases, the pulmonary stenosis 11 does not occur, the pulmonary trunk is markedly dilated as in figure 25 and there is a high vsd immediately subjacent to the pulmonary valve subpulmo.
Ebsteins anomaly is a congenital heart defect in which the septal and posterior leaflets of the tricuspid valve are displaced towards the apex of the right ventricle. Taussig bing anomaly named after the authors that first described it helen b. The syndrome was described by taussig and bing in 1949, pernkopf 1920. Taussigbing anomaly is a rare congenital heart malformation and is one of the variants of double outlet right ventricle it consists of transposition of the aorta to the right ventricle and malposition of the pulmonary artery with subpulmonary ventricular septal defect history and etymology. In the type called the taussig bing anomaly top right diagram 2 blood from the lv passes through the vsd to the pulmonary artery, whilst blood from the rv tends to be directed mainly to the aorta. Double outlet right ventricle dorv taussigbing malformation tetralogy of fallot with extreme dextroposition of the aorta eisenmengers anomaly eisenmenger ventricular septal defect european paediatric cardiac code reference of double outlet right ventricle is. Arterial switch versus kawashima intraventricular repair constantine mavroudis, md, carl l.
Page 4 of 15 1 aorta originating from rv 2 pulmonary artery in normal position and lies side by side with aorta. In these cases, the pulmonary stenosis 11 does not occur, the pulmonary trunk is markedly dilated as in figure 25 and there is a high vsd immediately subjacent to. Patients with taussigbing anomaly and aorticarch obstruction may have a higher reoperation rate than those with normalarch anatomy. Taussingbing anomaly, with or without aortic archobstruction, can be repaired with arterial switch operation during theneonatal period with good outcome. A bible for the 21st century combining traditional and newly discovered texts is the first one to be what publishers call a trade book. This means it is for a public audience by a major publisher that makes the book available in a wide variety of.
Throughout her career, taussig earned more than 20 honorary degrees. Taussigbing syndrome is a cyanotic congenital heart defect in which the patient has both double outlet right ventricle dorv and subpulmonic ventricular septal defect vsd in dorv, instead of the normal situation where blood from the left ventricle lv flows out to the aorta and blood from the right ventricle rv flows out to the pulmonary artery, both aorta and pulmonary artery are. Taussigbing anomaly and aortic arch obstruction are two types of complex congenital cardiac malformations. Rees, md, and melanie gevitz, ba divisions of cardiovascularthoracic surgery and cardiology, the childrens memorial hospital, and departments of surgery and pediatrics, northwestern university medical school. The characteristic feature of the taussig bing anomaly tba that makes. Taussigbing syndrome synonyms, taussigbing syndrome. From 1986 through july 2005, 34 patients with taussigbing anomaly underwent the arterial switch operation.
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